New Codes Choices for Corneal Dystrophy Proposed

Proposed new codes were introduced at the CMS Coordination and Maintenance Committee meeting.

The need for expanding the ICD-10-CM code choices for corneal dystrophy was a topic covered at the Centers for Medicare & Medicaid Services (CMS) ICD-10 Coordination and Maintenance Committee meeting in March when multiple new codes were proposed.

There are more than 20 types of corneal dystrophy. In the 2019 version of ICD-10-CM, there are only choices for nodular, other, unspecified, and hereditary, nullifying the coder’s ability to choose or drill down, as there are five layers in the cornea: the epithelium, the Bowman’s membrane, the stroma, the Descemet’s membrane, and the endothelium.

Clinically, corneal dystrophies can be divided into three groups, based on the anatomical location of the abnormality. Some affect primarily the corneal epithelium and its basement membrane, or Bowman layer, and others affect the superficial corneal stroma (or anterior corneal dystrophies), the corneal stroma (or Descemet membrane), and the corneal endothelium (or posterior corneal dystrophies). Many corneal dystrophies have no systemic manifestations. Macular corneal dystrophy and Schnyder corneal dystrophy do, though. Most corneal dystrophies affect both eyes and tend to run in families. They can appear at any age. Some are symptom-free and are found on routine eye exams.

Treatment depends on the type of dystrophy, as well as the severity of symptoms. Since the treatment depends on the type, types should be clearly available in the coding selections to take away the administrative burden of using a less specific choice and then fighting for coverage or benefits.

The American Academy of Ophthalmology requested new codes for hereditary, endothelial, granular, lattice, and macular dystrophies, and for complications due to transplant or transplant failure. These additions will help us better track outcomes and quality measurements. These selections also include laterality.

The proposal also pairs up with more offerings that are available in ICD-11. In ICD-11, there are choices for endothelial, dermochondrocorneal, dyslipoproteinaemic, choroidal, structural, congenital, tyrosinaemia type 2, and other dystrophies. “Other” encompasses granular, lattice, macular, stromal, and many other classifications. Interestingly enough, we actually lose some granularity in ICD-11 from the proposed breakdown in ICD-10-CM.

This is a good reminder that we have a long way to go in making clinical modifications that will be necessary for our use of the new coding classification in order for them to become most useful for our tracking and quality measures. I can’t imagine us embracing a coding system that actually takes us backward; instead, we will need to do the work required to make sure that our ICD-11 efforts are as robust as our ICD-10-CM efforts were, or it’s not worth making a transition.

There is also a chance to make sure our physician’s documentation is on point for the upcoming changes. We need to be forward-thinking in our planning. As a carpenter would say, “measure twice, cut once.” The same can apply to our documentation. If we turn to the many evidence-based guidelines for the various types of corneal dystrophy, we can then begin to document in a way that exceeds expectations in ICD-10 and also meets ICD-11 standards. As I have mentioned in past training and articles, the goals of good documentation should not be designed to meet coding requirements. Instead, focus your efforts on documenting for the appropriate condition through evidence-based medicine guidelines; you’ll more than meet any coding regulation or quality measure.

It’s frustrating to base our documentation on one code set and then try to bring it back or beef it up based on a new one. The patient’s clinical condition remains more or less the same, dependent on conditions being experienced. By focusing on this, you can take the administrative burden out of your documentation requirements.


Programming Note:

Listen to Rhonda Buckholtz report this story live today during Talk Ten Tuesday, 10-10:30 a.m. ET.

Facebook
Twitter
LinkedIn

Related Stories

Leave a Reply

Please log in to your account to comment on this article.

Featured Webcasts

Mastering Breast Biopsy Billing: Guidance-Driven Coding for Accurate Reimbursement

Breast biopsy procedures may be clinically straightforward but accurately translating them into compliant billing can be anything but. In this focused webcast, Shawn Blackburn, CPC, CPMA, CIC, CRC, CCS-P breaks down how imaging guidance, lesion count, laterality, and payer expectations all impact how these procedures should be reported. Through clear explanations and real-world scenarios, you’ll gain practical insight into aligning clinical workflows with billing requirements, avoiding common pitfalls, and ensuring your documentation supports accurate reimbursement and compliance.

May 21, 2026

Mastering OB GYN Coding Accuracy: Precision Coding for Compliance and Reimbursement

Gain clarity and confidence in OB‑GYN coding with this expert‑led webcast featuring Sherri L. Clayton, RHIT, CSS. You’ll learn how to apply global maternity package rules accurately, select the right CPT codes for procedures and visits, and identify documentation gaps that lead to denials. With practical guidance and real examples, this session helps you strengthen compliance, reduce audit risk, and ensure accurate reimbursement for women’s health services.

May 14, 2026

2026 ICD-10-CM/PCS Coding Clinic Update Webcast Series

Uncover essential coding insights with nationally recognized coding authority Kay Piper, RHIA, CDIP, CCS. Through ICD10monitor’s interactive, on‑demand webcast series, Kay walks you through the AHA’s 2026 ICD‑10‑CM/PCS Quarterly Coding Clinics, translating each update into practical, easy‑to‑apply guidance designed to sharpen precision, ensure compliance, and strengthen day‑to‑day decision‑making. Available shortly after each official release.

April 13, 2026

2026 ICD-10-CM/PCS Coding Clinic Update: Fourth Quarter

Uncover critical guidance on the ICD-10-CM/PCS code updates. Kay Piper reviews and explains ICD-10-CM/PCS coding guidelines in the AHA’s fourth quarter 2026 ICD-10-CM/PCS Coding Clinic in an easy to access on-demand webcast.

December 14, 2026

Trending News

Featured Webcasts

Reengineering Utilization Management: Building an Adaptive Model for the New Payer Era

Traditional utilization management models can no longer keep pace with regulatory shifts, payer scrutiny, and operational pressures. In this webcast, Tiffany Ferguson, LMSW, CMAC, ACM, ACPA-C, introduces an Adaptive Model strategy that modernizes UM through role specialization, technology-driven workflows, and proactive, team-based processes. Attendees will learn how to restructure programs to improve efficiency, strengthen clinical collaboration, and enhance financial performance in a rapidly changing healthcare environment.

May 20, 2026

Compliance for the Inpatient Psychiatric Facility (IPF-PPS): Minimizing Federal Audit Findings by Strengthening Best Practices

Federal auditors are intensifying their focus on inpatient psychiatric facilities, using advanced data analytics to spotlight outliers and pursue high‑dollar repayments. In this high‑impact webcast, Michael Calahan, PA, MBA, Compliance Officer and V.P., Hospital & Physician Compliance, breaks down what regulators are really targeting in IPF-PPS admissions, documentation, treatment and discharge planning. Attendees will learn practical steps to tighten processes, avoid common audit triggers and protect reimbursement and reduce the risk of multimillion-dollar repayment demands.

April 9, 2026

Mastering MDM for Accurate Professional Fee Coding

In this timely session, Stacey Shillito, CDIP, CPMA, CCS, CCS-P, CPEDC, COPC, breaks down the complexities of Medical Decision Making (MDM) documentation so providers can confidently capture the true complexity of their care. Attendees will learn practical, efficient strategies to ensure documentation aligns with current E/M guidelines, supports accurate coding, and reduces audit risk, all without adding to charting time.

March 31, 2026

The PEPPER Returns – Risk and Opportunity at Your Fingertips

Join Ronald Hirsch, MD, FACP, CHCQM for The PEPPER Returns – Risk and Opportunity at Your Fingertips, a practical webcast that demystifies the PEPPER and shows you how to turn complex claims data into actionable insights. Dr. Hirsch will explain how to interpret key measures, identify compliance risks, uncover missed revenue opportunities, and understand new updates in the PEPPER, all to help your organization stay ahead of audits and use this powerful data proactively.

March 19, 2026

Trending News

Happy HIP Week! Sign up to win free access to our 2026 Coding Clinic Update Webcast Series! Click here to learn more →

Prepare for the 2025 CMS IPPS Final Rule with ICD10monitor’s IPPSPalooza! Click HERE to learn more

Get 15% OFF on all educational webcasts at ICD10monitor with code JULYFOURTH24 until July 4, 2024—start learning today!

CYBER WEEK IS HERE! Don’t miss your chance to get 20% off now until Dec. 1 with code CYBER25

CYBER WEEK IS HERE! Don’t miss your chance to get 20% off now until Dec. 2 with code CYBER24